EXTROPHIE VESICALE PDF

Request PDF on ResearchGate | On Jun 1, , S. Jochault-Ritz and others published CL – Qualité de vie dans l’exstrophie vésicale, résultats de l’étude. Malformation: extrophie vésicale has members. Parents Group. Website; Head of organisation: Mr Philip ANDERMATT; Vereinigung Blasenexstrophie – Association Exstrophie Vésicale – Associazione Estrofia Vesicale.

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Other search option s Alphabetical list. Video about the HONcode. Disease definition Exstrophy-Epispadias Complex EEC represents a spectrum of genitourinary malformations vesicake in severity from epispadias E and classical bladder exstrophy Extroohie to exstrophy of the cloaca EC as the most severe form see these terms. In puberty, genital and reproductive functions constitute increasingly important issues for both sexes. Detailed information Professionals Review article English Management and treatment Management is primarily surgical, with the main aims of obtaining secure abdominal wall closure, achieving urinary continence with preservation of renal function, and, finally, adequate cosmetic and functional genital reconstruction.

Etiology The underlying cause remains unknown: Health website editors Do you have your own website? The underlying cause remains unknown: In cases of definite reconstruction failure, urinary diversion should be undertaken. For all other comments, please send your remarks via contact us. The HONcode toolbar is easy to download and add to your Web browser.

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However, despite the complaint system that has been put in place and the periodic review and automatic monitoring of certified sites to ensure maximum compliance with the HONcode ethical principles, it is impossible to eliminate all risks of incoherence that may vewicale. Only comments written in English can be processed. The timing of the rupture determines the severity of the malformation. Those responsible for the certified website are responsible for the content of the website unless otherwise provided by law.

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Genetic counseling Extensive counseling should be provided to parents but due to a generally favorable outcome with appropriate surgical management, termination of the pregnancy should no longer be systematically recommended. Health information you can trust! Clinical description EEC is characterized by a visible defect of the lower abdominal wall, either with an evaginated bladder plate CEBor with an open urethral plate in males or a cleft in females E.

EEC is characterized by a visible defect of the lower abdominal wall, either with an evaginated bladder plate CEBor with an open urethral plate in males or vesivale cleft in females E.

Journal de la Recherche Scientifique de l’Université de Lomé

In the rare cases of CE, two exstrophied hemibladders, as well as omphalocele, an imperforate anus and spinal defects, can be seen after birth. Providing you with trustworthy health information. Data di rassegna iniziale: Check this box if you wish to receive a copy of your message. The documents contained in this web site are presented for information purposes only. Extensive counseling should be provided to parents but due to a generally favorable outcome with appropriate surgical management, termination of the pregnancy should no longer be systematically recommended.

Atypical forms of the EEC duplicated exstrophy, covered exstrophy and pseudo-exstrophy have also been described. Diagnosis at birth is made on the basis of the clinical presentation but EEC may be detected prenatally during careful ultrasound examinations with the index finding of repeated non-visualization of a normally filled fetal bladder. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted.

Diagnostic methods Diagnosis at birth is made on the basis of the clinical presentation but EEC may be detected prenatally during careful ultrasound examinations with the index finding of repeated non-visualization of a normally filled fetal bladder. It connects in real time to the HON server to verify the certification status of health and medical websites. Download the free HONcode toolbar.

Depending on severity, the EEC may involve the urinary system, the musculoskeletal system, the pelvis, the pelvic floor, the abdominal wall, the genitalia and sometimes the spine and the anus.

Management is primarily surgical, with the main aims of obtaining secure abdominal wall closure, achieving urinary continence with preservation of renal function, and, finally, adequate cosmetic and functional genital reconstruction.

EEC results from mechanical disruption or enlargement of the cloacal membrane, which prevents the invasion of mesodermal cells along the infraumbilical midline and thereby results in exstrophy.

Exstrophy-Epispadias Complex EEC represents a spectrum of genitourinary malformations ranging in severity from epispadias E and classical bladder exstrophy CEB to exstrophy of the cloaca EC as the most severe form see these terms. Summary and related texts.

Orphanet: Exstrophie vesicale epispadias

The data displayed correspond to only one of the selected samples. Health care resources for this disease Expert centres Diagnostic tests 3 Patient organisations 30 Orphan drug s 0.

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Psychosocial and psychosexual outcome reflect the importance of long-term care from birth into adulthood from a multidisciplinary team of experts for parents and children with EEC to facilitate an adequate quality exhrophie life. Urine drips from the ureteric orifices, visible on the bladder surface or per urethram. NeonatalAntenatal ICD The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.